歯学ジャーナル
オープンアクセス

概要

Prophylactic Treatments for Retinal Tears/Detachment in Stickler Syndrome: Single Institution Experience

Kiran Turaka, J. Shepard Bryan, Alan J. Gordon, Matthew C. Ziemianski, and Clive H. Sell

Background: To report the clinical features and prophylactic treatment methods for retinal pathology in Stickler syndrome (SS) patients (pts).
Methods: A retrospective non-comparative interventional case series.
Results: The median age of the pts was 12 (range 0.2-68) years. Systemic features of SS were present in 23 pts. High myopia was present in 19 pts. Treatment was by laser retinopexy and or cryotherapy (n=15) and vitrectomy plus scleral buckle (SB) (n=6). Five fellow eyes with extensive lattice degeneration with or without associated retinal tears treated by prophylactic SB. The median follow-up was 65.5 months (range 5-226). Seven fellow eyes developed RD over a median duration of 22.5 (range 5-123) months, who were treated by vitrectomy plus SB (n=6) and vitrectomy, silicon oil and laser retinopexy (n=1).
Conclusions: Prophylactic treatments such scleral buckle and laser and cryotherapy prevented the development of retinal tears or detachment in pts with Stickler syndrome.