リウマチ学: 現在の研究
オープンアクセス

概要

Pseudo-Tumoral Cerebral Involvement during Behcet’s Disease

Amira Atig, Maissa Thabet*, Ahmed Guiga, Wissal Ben Yahia, Neirouz Ghannouchi

Neurological pseudo-tumoral presentation of Behcet’s disease is rarely observed. We report the case of 23-year-old men who presented with temporo-spatial disorientation. He has also, bipolar aphtosis, right peripherical facial paralysis and ptosis. There was neither fever nor lymphadenopathies on the examination. Ophthalmological examination had objectified bilateral anterior uveitis. Serological tests and autoimmunity study were normal. The brain angio-Magnetic Resonance Imaging (MRI) showed intra parenchymal infiltrative lesion affecting right capsulothalamic region and the protuberance. The diagnosis of pseudo-tumoral Neuro-Behcet's Disease (NBD) is suspected. Treatment with corticosteroids and cyclophosphamide had improved clinical and radiological outcome after a 3-years follow-up. A history of recurrent oral and genital ulcers since 2 years, the clinical context and the significant response to steroids, confirmed that the brain mass is related to Neuro-Behcet's Disease (NBD).