リウマチ学: 現在の研究
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概要

Vasodilatory Therapeutics in the Pulmonary Hypertension Assessment and Recognition of Outcomes in Scleroderma (PHAROS) Cohort

Tracy Frech, Jessica Gordon, Lorinda Chung, Marcy Bolster, Barbara Segal, Ann Impens, Lee Shapiro, Avram Goldberg, Vivien Hsu, Chris T Derk, Dinesh Khanna, Monique Hinchcliff, Maureen A Murtaugh and Virginia Steen

The Pulmonary Hypertension Assessment and Recognition of Outcomes in Scleroderma (PHAROS) registry was designed to advance the understanding of the pathogenesis of pulmonary arterial hypertension (PAH) in systemic sclerosis (SSc). This registry provides the opportunity to examine both microvascular and macrovascular complications in SSc. In this manuscript we review SSc-PAH therapies and report on their use in the PHAROS registry.