泌尿器科・外科
オープンアクセス

概要

Bi-Focal Retroperitoneal Paraganglioma in a Young Patient: A Case Report and Review of the Literature

Ksenija Limani, Roland Van Velthoven and Fouad Aoun

Extra-adrenal paraganglioma of the retroperitoneum are rare neuroendocrine tumors arising from specialized neural crest cells, intimately associated with sympathetic nervous tissue and distributed along the aorta. Here we present a case of multiple extra-adrenal retroperitoneal paraganglioma in a 16-year-old boy. The clinical presentation, imaging characteristics, and surgical pathologic findings were reported. A comprehensive review of the medical literature concerning multiple extra-adrenal paraganglioma in the pediatric and adult population is also discussed.